BACK TOTOP Browse A-ZSearchBrowse A-ZABCDEFGHIJKLMNOPQRSTUVWXYZ0-9 E-mail FormEmail ResultsName:Email address:Recipients Name:Recipients address:Message: Print-FriendlyBookmarksbookmarks-menuCraniosynostosisPremature closure of sutures; Synostosis; Plagiocephaly; Scaphocephaly; Fontanelle - craniosynostosis; Soft spot - craniosynostosisCraniosynostosis is a birth defect in which one or more sutures on a baby's head closes earlier than usual.The skull of an infant or young child is made up of bony plates that are still growing. The borders at which these plates intersect are called sutures or suture lines. The sutures allow for growth of the skull. They normally close ("fuse") by the time the child is 2 or 3 years old.Early closing of a suture causes the baby to have an abnormally shaped head. This may limit brain growth. Causes The cause of craniosynostosis is not known. Genes may play a role, but there is usually no family history of the condition. It may be caused by external pressure on a baby's head before birth. Abnormal development of the base of the skull and the membranes around the skull bones is believed to affect the movement and position of the bones as they grow.In cases when this is passed down through families, it may occur with other health problems, such as seizures, decreased intelligence, and blindness. Genetic disorders commonly linked to craniosynostosis include Crouzon, Apert, Carpenter, Saethre-Chotzen, and Pfeiffer syndromes.However, most children with craniosynostosis are otherwise healthy and have normal intelligence. Symptoms Symptoms depend on the type of craniosynostosis. They may include:No "soft spot" (fontanelle) on the newborn's skull A raised hard ridge along the affected sutures Unusual head shape Slow or no increase in the head size over time as the baby growsTypes of craniosynostosis are:Sagittal synostosis (scaphocephaly) is the most common type. It affects the main suture on the very top of the head. The early closing forces the head to grow long and narrow, instead of wide. Babies with this type tend to have a broad forehead. It is more common in boys than girls. Frontal plagiocephaly is the next most common type. It affects the suture that runs from ear to ear on the top of the head. It usually occurs on just one side, causing a flattened forehead, raised eyebrow, and prominent ear on that side. The baby's nose may also appear to be pulled toward that side. This is more common in girls than in boys. Metopic synostosis is a rare form that affects the suture close to the forehead. The child's head shape may be described as trigonocephaly, because the top of the head appears triangular, with a narrow or pointed forehead. It may range from mild to severe. Exams and Tests The health care provider will feel the infant's head and perform a physical exam.The following tests may be done:Measuring the circumference of the infant's head X-rays of the skull X-raysA skull x-ray is a picture of the bones surrounding the brain, including the facial bones, the nose, and the sinuses.ImageRead Article Now Book Mark Article CT scan of the headCT scanA head computed tomography (CT) scan uses many x-rays to create pictures of the head, including the skull, brain, eye sockets, and sinuses.ImageRead Article Now Book Mark Article Well-child visits are an important part of your child's health care. They allow the provider to regularly check the growth of your infant's head over time. This will help identify any problems early. Treatment Surgery is usually needed. It is done while the baby is still an infant. The goals of surgery are:Relieve any pressure on the brain. Make sure there is enough room in the skull to allow the brain to properly grow. Improve the appearance of the child's head. Outlook (Prognosis) How well a child does depends on:How many sutures are involved The child's overall health Children with this condition who have surgery do well in most cases, especially when the condition is not associated with a genetic syndrome. Possible Complications Craniosynostosis results in head deformity that can be severe and permanent if it is not corrected. Complications may include:Increased intracranial pressure Seizures Developmental delay When to Contact a Medical Professional Call your child's provider if your child has:Unusual head shape Problems with growth Unusual raised ridges on the skullOpen ReferencesReferencesCenters for Disease Control and Prevention website. Facts about craniosynostosis. www.cdc.gov/ncbddd/birthdefects/craniosynostosis.html . Updated October 23, 2020. Accessed January 19, 2022.Graham JM, Sanchez-Lara PA. Craniosynostosis: general. In: Graham JM, Sanchez-Lara PA, eds. Smith's Recognizable Patterns of Human Deformation. 4th ed. Philadelphia, PA: Elsevier; 2016:chap 29.Kinsman SL, Johnston MV. Congenital anomalies of the central nervous system. In: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Textbook of Pediatrics. 21st ed. Philadelphia, PA: Elsevier; 2020:chap 609.Mandela R, Bellew M, Chumas P, Nash H. Impact of surgery timing for craniosynostosis on neurodevelopmental outcomes: a systematic review. J Neurosurg Pediatr. 2019;23(4):442-454. PMID: 30684935 pubmed.ncbi.nlm.nih.gov/30684935/.AllVideoImagesTogSkull of a newborn - illustration The sutures or anatomical lines where the bony plates of the skull join together can be easily felt in the newborn infant. The diamond shaped space on the top of the skull and the smaller space further to the back are often referred to as the soft spot in young infants.Skull of a newbornillustrationSkull of a newborn - illustration The sutures or anatomical lines where the bony plates of the skull join together can be easily felt in the newborn infant. The diamond shaped space on the top of the skull and the smaller space further to the back are often referred to as the soft spot in young infants.Skull of a newbornillustrationRelated Information Craniosynostosis repair(Surgery)Craniosynostosis repair - discharge (Discharge) Review Date: 11/9/2021 Reviewed By: Kimberly G Lee, MD, MSc, IBCLC, Clinical Professor of Pediatrics, Division of Neonatology, Medical University of South Carolina, Charleston, SC. Review provided by VeriMed Healthcare Network. Also reviewed by David Zieve, MD, MHA, Medical Director, Brenda Conaway, Editorial Director, and the A.D.A.M. Editorial team. 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